Saudi Journal of Medicine and Medical Sciences

CASE REPORT
Year
: 2014  |  Volume : 2  |  Issue : 1  |  Page : 52--56

Unusual presentation of kimura俟Q製 disease


Amol W Diwan, Gauri P Godbole, Himanshu S Pophale, Suhas R Kulkarni 
 Department of Pulmonary Medicine, Smt. Kashibai Navale Medical College and General Hospital, Narhe, Pune, Maharashtra, India

Correspondence Address:
Amol W Diwan
Department of Pulmonary Medicine, Smt. Kashibai Navale Medical College and General Hospital, Off Pune-Banglore Highway, Narhe, Pune - 411 041, Maharashtra
India

Kimura俟Q製 disease is a rare form of chronic eosinophilic inflammatory disorder with associated lymphadenopathy in head and neck region and serous cavity effusions and marked predilection for the head and neck with a tendency to present as a discrete, enlarging mass. Although many cases of Kimura俟Q製 disease with head and neck lymphadenopathy and nephrotic syndrome have been described in the literature, only two cases of Kimura俟Q製 disease presenting with pleural effusion have been reported recently. There are no reports of Kimura俟Q製 disease with ascites. We report the case of a 38-year-old nondiabetic, normotensive man who had undergone inguinal node biopsy consistent with Kimura俟Q製 disease, 8 months before he presented to us. On admission, he had right moderate pleural effusion, but no ascites or any lymph nodal involvement. He developed recurrent pleural effusion and ascites in the ward. Initially he showed good remission with systemic steroids, but later on was refractory to further necessary treatment. He also rapidly developed signs of nephrotic syndrome. In spite of vigorous treatment, patient died of severe hypovolemia, hypoproteinemia, and nephropathy.


How to cite this article:
Diwan AW, Godbole GP, Pophale HS, Kulkarni SR. Unusual presentation of kimura's disease.Saudi J Med Med Sci 2014;2:52-56


How to cite this URL:
Diwan AW, Godbole GP, Pophale HS, Kulkarni SR. Unusual presentation of kimura's disease. Saudi J Med Med Sci [serial online] 2014 [cited 2021 Mar 8 ];2:52-56
Available from: https://www.sjmms.net/article.asp?issn=1658-631X;year=2014;volume=2;issue=1;spage=52;epage=56;aulast=Diwan;type=0